Thomas Jefferson University

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Uitto, Jouni
One or more keywords matched the following items that are connected to Uitto, Jouni
Item TypeName
Concept Animals
Concept Animal Feed
Concept Animal Structures
Concept Animals, Newborn
Concept Disease Models, Animal
Concept Models, Animal
Concept Animals, Genetically Modified
Concept Animal Nutrition Sciences
Academic Article Overexpression of fetuin-a counteracts ectopic mineralization in a mouse model of pseudoxanthoma elasticum (abcc6(-/-)).
Academic Article Parabiotic heterogenetic pairing of Abcc6-/-/Rag1-/- mice and their wild-type counterparts halts ectopic mineralization in a murine model of pseudoxanthoma elasticum.
Academic Article Magnesium carbonate-containing phosphate binder prevents connective tissue mineralization in Abcc6(-/-) mice-potential for treatment of pseudoxanthoma elasticum.
Academic Article Animal models of epidermolysis bullosa: update 2010.
Academic Article The abcc6a gene expression is required for normal zebrafish development.
Academic Article Zebrafish type XVII collagen: gene structures, expression profiles, and morpholino "knock-down" phenotypes.
Academic Article Gene expression signatures of mouse bone marrow-derived mesenchymal stem cells in the cutaneous environment and therapeutic implications for blistering skin disorder.
Academic Article Angioid streaks in Pseudoxanthoma Elasticum: role of the p.R1268Q mutation in the ABCC6 gene.
Academic Article Zebrafish: a model system to study heritable skin diseases.
Academic Article Revertant mosaicism in skin: natural gene therapy.
Academic Article Administration of vitamin K does not counteract the ectopic mineralization of connective tissues in Abcc6 (-/-) mice, a model for pseudoxanthoma elasticum.
Academic Article Regenerative medicine for skin diseases: iPS cells to the rescue.
Academic Article The Samd9L gene: transcriptional regulation and tissue-specific expression in mouse development.
Academic Article Expression of the Abca-subfamily of genes in Abcc6-/- mice--upregulation of Abca4.
Academic Article Pseudoxanthoma elasticum, the paradigm of heritable ectopic mineralization disorders - can diet help?
Academic Article PDGFRalpha-positive cells in bone marrow are mobilized by high mobility group box 1 (HMGB1) to regenerate injured epithelia.
Academic Article Pseudoxanthoma elasticum: progress in diagnostics and research towards treatment : Summary of the 2010 PXE International Research Meeting.
Academic Article ABCC6 does not transport adenosine - relevance to pathomechanism of pseudoxanthoma elasticum.
Academic Article Abca12-mediated lipid transport and Snap29-dependent trafficking of lamellar granules are crucial for epidermal morphogenesis in a zebrafish model of ichthyosis.
Academic Article ABCC6 does not transport vitamin K3-glutathione conjugate from the liver: relevance to pathomechanisms of pseudoxanthoma elasticum.
Academic Article Connective tissue mineralization in Abcc6-/- mice, a model for pseudoxanthoma elasticum.
Academic Article Magnesium reduces carotid intima-media thickness in a mouse model of pseudoxanthoma elasticum: a novel treatment biomarker.
Academic Article A novel animal model for pseudoxanthoma elasticum: the KK/HlJ mouse.
Academic Article Specific sequences in p120ctn determine subcellular distribution of its multiple isoforms involved in cellular adhesion of normal and malignant epithelial cells.
Academic Article Interspecies conservation and differential expression of mouse desmoglein gene family.
Academic Article Loss of cell adhesion in Dsg3bal-Pas mice with homozygous deletion mutation (2079del14) in the desmoglein 3 gene.
Academic Article Desmoglein 4 in hair follicle differentiation and epidermal adhesion: evidence from inherited hypotrichosis and acquired pemphigus vulgaris.
Academic Article Procollagen VII self-assembly depends on site-specific interactions and is promoted by cleavage of the NC2 domain with procollagen C-proteinase.
Academic Article Targeted inactivation of murine laminin gamma2-chain gene recapitulates human junctional epidermolysis bullosa.
Academic Article Transcriptional control of the mouse Col7a1 gene in keratinocytes: basal and transforming growth factor-beta regulated expression.
Academic Article Periplakin gene targeting reveals a constituent of the cornified cell envelope dispensable for normal mouse development.
Academic Article Single amino acid substitutions in procollagen VII affect early stages of assembly of anchoring fibrils.
Academic Article Differential structural properties and expression patterns suggest functional significance for multiple mouse desmoglein 1 isoforms.
Academic Article Breaking the connection: caspase 6 disconnects intermediate filament-binding domain of periplakin from its actin-binding N-terminal region.
Academic Article Animal models of epidermolysis bullosa--targets for gene therapy.
Academic Article A simplified laminin nomenclature.
Academic Article Extracellular matrix protein 1 interacts with the domain III of fibulin-1C and 1D variants through its central tandem repeat 2.
Academic Article Targeted ablation of the abcc6 gene results in ectopic mineralization of connective tissues.
Academic Article The Ehlers-Danlos syndrome--phenotypic spectrum and molecular genetics.
Academic Article Tissue-specific expression of the ABCC6 gene.
Academic Article Transcriptional regulation and characterization of the promoter region of the human ABCC6 gene.
Academic Article Lung development in laminin gamma2 deficiency: abnormal tracheal hemidesmosomes with normal branching morphogenesis and epithelial differentiation.
Academic Article Aberrant mineralization of connective tissues in a mouse model of pseudoxanthoma elasticum: systemic and local regulatory factors.
Academic Article Suprabasal Dsg2 expression in transgenic mouse skin confers a hyperproliferative and apoptosis-resistant phenotype to keratinocytes.
Academic Article Diseases of epidermal keratins and their linker proteins.
Academic Article Targeted ablation of Abcc1 or Abcc3 in Abcc6(-/-) mice does not modify the ectopic mineralization process.
Academic Article Development of tissue-targeting hemagglutinating virus of Japan envelope vector for successful delivery of therapeutic gene to mouse skin.
Academic Article Pseudoxanthoma elasticum: reduced gamma-glutamyl carboxylation of matrix gla protein in a mouse model (Abcc6-/-).
Academic Article Ectopic mineralization of connective tissue in Abcc6-/- mice: effects of dietary modifications and a phosphate binder--a preliminary study.
Academic Article Pseudoxanthoma elasticum: oxidative stress and antioxidant diet in a mouse model (Abcc6-/-).
Academic Article Comparison of 1D and 2D NMR spectroscopy for metabolic profiling.
Academic Article Mice deficient in involucrin, envoplakin, and periplakin have a defective epidermal barrier.
Academic Article The role of elastin and collagen in cutaneous aging: intrinsic aging versus photoexposure.
Academic Article Collagen fibril formation. A new target to limit fibrosis.
Academic Article Pseudoxanthoma elasticum is a metabolic disease.
Academic Article Bone marrow cell transfer into fetal circulation can ameliorate genetic skin diseases by providing fibroblasts to the skin and inducing immune tolerance.
Academic Article Mutations in the GGCX and ABCC6 genes in a family with pseudoxanthoma elasticum-like phenotypes.
Academic Article Amelioration of epidermolysis bullosa by transfer of wild-type bone marrow cells.
Academic Article Injection of recombinant human type VII collagen corrects the disease phenotype in a murine model of dystrophic epidermolysis bullosa.
Academic Article Pseudoxanthoma elasticum: clinical phenotypes, molecular genetics and putative pathomechanisms.
Academic Article Elevated dietary magnesium prevents connective tissue mineralization in a mouse model of pseudoxanthoma elasticum (Abcc6(-/-)).
Academic Article Molecular therapies for heritable blistering diseases.
Academic Article The mineralization phenotype in Abcc6 ( -/- ) mice is affected by Ggcx gene deficiency and genetic background--a model for pseudoxanthoma elasticum.
Academic Article Keratinocyte-/fibroblast-targeted rescue of Col7a1-disrupted mice and generation of an exact dystrophic epidermolysis bullosa model using a human COL7A1 mutation.
Academic Article Noninvasive assessment of UV-induced skin damage: comparison of optical measurements to histology and MMP expression.
Academic Article Pseudoxanthoma elasticum: molecular genetics and putative pathomechanisms.
Academic Article Keloids: Animal models and pathologic equivalents to study tissue fibrosis.
Academic Article Misbalanced CXCL12 and CCL5 Chemotactic Signals in Vitiligo Onset and Progression.
Academic Article Abcc6 Knockout Rat Model Highlights the Role of Liver in PPi Homeostasis in Pseudoxanthoma Elasticum.
Academic Article Inherited human ITK deficiency impairs IFN-? immunity and underlies tuberculosis.
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