"Neurofibrosarcoma" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
A malignant tumor that arises from small cutaneous nerves, is locally aggressive, and has a potential for metastasis. Characteristic histopathologic features include proliferating atypical spindle cells with slender wavy and pointed nuclei, hypocellular areas, and areas featuring organized whorls of fibroblastic proliferation. The most common primary sites are the extremities, retroperitoneum, and trunk. These tumors tend to present in childhood, often in association with NEUROFIBROMATOSIS 1. (From DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p1662; Mayo Clin Proc 1990 Feb;65(2):164-72)
| Descriptor ID |
D018319
|
| MeSH Number(s) |
C04.557.450.565.590.350.590 C04.557.450.795.350.590 C04.557.580.600.580.795 C10.551.775.500.750.750 C10.668.829.725.500.600.600
|
| Concept/Terms |
Neurofibrosarcoma- Neurofibrosarcoma
- Neurofibrosarcomas
- Sarcoma, Neurogenic
- Neurogenic Sarcoma
- Neurogenic Sarcomas
- Sarcomas, Neurogenic
|
Below are MeSH descriptors whose meaning is more general than "Neurofibrosarcoma".
Below are MeSH descriptors whose meaning is more specific than "Neurofibrosarcoma".
This graph shows the total number of publications written about "Neurofibrosarcoma" by people in this website by year, and whether "Neurofibrosarcoma" was a major or minor topic of these publications.
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| Year | Major Topic | Minor Topic | Total |
|---|
| 2018 | 1 | 0 | 1 |
| 2019 | 2 | 0 | 2 |
| 2021 | 1 | 0 | 1 |
| 2022 | 1 | 0 | 1 |
| 2023 | 1 | 0 | 1 |
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Below are the most recent publications written about "Neurofibrosarcoma" by people in Profiles.
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Miettinen M, Abdullaev Z, Turakulov R, Quezado M, Lui?a Contreras A, Curcio CA, Rys J, Chlopek M, Lasota J, Aldape KD. Assessment of The Utility of The Sarcoma DNA Methylation Classifier In Surgical Pathology. Am J Surg Pathol. 2024 Jan 01; 48(1):112-122.
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Gambarotti M, Righi A, Sbaraglia M, Cocchi S, Benini S, Magagnoli G, Frisoni T, Palmerini E, Picci P, Dei Tos AP. Primary malignant peripheral nerve sheath tumors of bone: a clinicopathologic reappraisal of 8 cases. Hum Pathol. 2022 04; 122:92-102.
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Aplin AE, Capparelli C. Combined SHPments: An Effective Therapeutic Strategy for MPNST. Cancer Res. 2021 01 15; 81(2):266-267.
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Benini S, Gamberi G, Cocchi S, Righi A, Frisoni T, Longhi A, Gambarotti M. Identification of a novel fusion transcript EWSR1-VEZF1 by anchored multiplex PCR in malignant peripheral nerve sheath tumor. Pathol Res Pract. 2020 Jan; 216(1):152760.
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Pemov A, Hansen NF, Sindiri S, Patidar R, Higham CS, Dombi E, Miettinen MM, Fetsch P, Brems H, Chandrasekharappa SC, Jones K, Zhu B, Wei JS, Mullikin JC, Wallace MR, Khan J, Legius E, Widemann BC, Stewart DR. Low mutation burden and frequent loss of CDKN2A/B and SMARCA2, but not PRC2, define premalignant neurofibromatosis type 1-associated atypical neurofibromas. Neuro Oncol. 2019 08 05; 21(8):981-992.
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Higham CS, Dombi E, Rogiers A, Bhaumik S, Pans S, Connor SEJ, Miettinen M, Sciot R, Tirabosco R, Brems H, Baldwin A, Legius E, Widemann BC, Ferner RE. The characteristics of 76 atypical neurofibromas as precursors to neurofibromatosis 1 associated malignant peripheral nerve sheath tumors. Neuro Oncol. 2018 05 18; 20(6):818-825.