Lymphohistiocytosis, Hemophagocytic

"Lymphohistiocytosis, Hemophagocytic" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus, MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure, which enables searching at various levels of specificity.

MeSH information

Definition | Details | More General Concepts | Related Concepts | More Specific Concepts

A group of related disorders characterized by LYMPHOCYTOSIS; HISTIOCYTOSIS; and hemophagocytosis. The two major forms are familial and reactive.

Descriptor ID	D051359
MeSH Number(s)	C15.604.250.410.575
Concept/Terms	Lymphohistiocytosis, Hemophagocytic Lymphohistiocytosis, Hemophagocytic Hemophagocytic Lymphohistiocytoses Hemophagocytic Lymphohistiocytosis Lymphohistiocytoses, Hemophagocytic Hemophagocytic Syndromes Hemophagocytic Syndrome Familial Hemophagocytic Lymphocytosis Familial Hemophagocytic Lymphocytosis Familial Hemophagocytic Lymphocytoses Hemophagocytic Lymphocytoses, Familial Hemophagocytic Lymphocytosis, Familial Lymphocytoses, Familial Hemophagocytic Lymphocytosis, Familial Hemophagocytic Familial Erythrophagocytic Lymphohistiocytosis Familial Histiocytic Reticulosis Familial Histiocytic Reticuloses Histiocytic Reticuloses, Familial Histiocytic Reticulosis, Familial Reticuloses, Familial Histiocytic Hemophagocytic Lymphohistiocytosis Familial -1 Hemophagocytic Lymphohistiocytosis Familial 1 Hemophagocytic Lymphohistiocytosis, Familial Familial Hemophagocytic Lymphohistiocytoses Hemophagocytic Lymphohistiocytoses, Familial Lymphohistiocytoses, Familial Hemophagocytic Lymphohistiocytosis, Familial Hemophagocytic Primary Hemophagocytic Hymphohistiocytosis Hemophagocytic Hymphohistiocytoses, Primary Hemophagocytic Hymphohistiocytosis, Primary Hymphohistiocytoses, Primary Hemophagocytic Hymphohistiocytosis, Primary Hemophagocytic Primary Hemophagocytic Hymphohistiocytoses Hemophagocytic Reticulosis, Familial Familial Hemophagocytic Reticuloses Hemophagocytic Reticuloses, Familial Reticuloses, Familial Hemophagocytic Reticulosis, Familial Hemophagocytic Primary Hemophagocytic Lymphohistiocytosis Hemophagocytic Lymphohistiocytoses, Primary Hemophagocytic Lymphohistiocytosis, Primary Lymphohistiocytoses, Primary Hemophagocytic Lymphohistiocytosis, Primary Hemophagocytic Primary Hemophagocytic Lymphohistiocytoses Reticulosis, Familial Histiocytic Familial Hemophagocytic Lymphohistiocytosis Familial Hemophagocytic Histiocytosis Familial Hemophagocytic Histiocytoses Hemophagocytic Histiocytoses, Familial Hemophagocytic Histiocytosis, Familial Histiocytoses, Familial Hemophagocytic Histiocytosis, Familial Hemophagocytic Familial Hemophagocytic Reticulosis Erythrophagocytic Lymphohistiocytosis, Familial Erythrophagocytic Lymphohistiocytoses, Familial Familial Erythrophagocytic Lymphohistiocytoses Lymphohistiocytoses, Familial Erythrophagocytic Lymphohistiocytosis, Familial Erythrophagocytic Hemophagocytic Lymphohistiocytosis, Familial, 1 Reactive Hemophagocytic Syndrome Reactive Hemophagocytic Syndrome Hemophagocytic Syndrome, Reactive Hemophagocytic Syndrome, Infection-Associated Hemophagocytic Syndrome, Infection Associated Infection-Associated Hemophagocytic Syndrome

Below are MeSH descriptors whose meaning is more general than "Lymphohistiocytosis, Hemophagocytic".

Diseases [C]
Hemic and Lymphatic Diseases [C15]
Lymphatic Diseases [C15.604]
Histiocytosis [C15.604.250]
Histiocytosis, Non-Langerhans-Cell [C15.604.250.410]
Lymphohistiocytosis, Hemophagocytic [C15.604.250.410.575]

Below are MeSH descriptors whose meaning is related to "Lymphohistiocytosis, Hemophagocytic".

Below are MeSH descriptors whose meaning is more specific than "Lymphohistiocytosis, Hemophagocytic".

publications

Timeline | Most Recent

This graph shows the total number of publications written about "Lymphohistiocytosis, Hemophagocytic" by people in this website by year, and whether "Lymphohistiocytosis, Hemophagocytic" was a major or minor topic of these publications.

Bar chart showing 25 publications over 13 distinct years, with a maximum of 4 publications in 2018 and 2023

To see the data from this visualization as text, click here.

Year	Major Topic	Minor Topic	Total
2005	1	0	1
2007	2	0	2
2010	2	0	2
2011	1	0	1
2013	1	0	1
2015	1	0	1
2016	3	0	3
2017	2	0	2
2018	4	0	4
2020	2	0	2
2021	0	1	1
2023	4	0	4
2024	1	0	1

Below are the most recent publications written about "Lymphohistiocytosis, Hemophagocytic" by people in Profiles.

Borda M, Tian H, Benitez S, Bonheur A, Dalvi N, Fraint E. Pediatric CNS-isolated hemophagocytic lymphohistiocytosis with brain hemorrhages: a case report. BMC Neurol. 2024 Oct 21; 24(1):404.

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Miyoshi Y, Kise T, Morita K, Okada H, Imadome KI, Tsuchida N, Maeda A, Uchiyama Y, Kirino Y, Matsumoto N, Yokogawa N. Long-term remission of?VEXAS syndrome achieved by a single course of?CHOP therapy: A case report. Mod Rheumatol Case Rep. 2023 12 29; 8(1):199-204.

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Manini N, Davidow K, Conard K, Powell J. Hematopoietic Bone Marrow Transplant to Treat Systemic EBV-positive T-cell Lymphoma of Childhood. J Pediatr Hematol Oncol. 2024 03 01; 46(2):e208-e211.

View in: PubMed
Gooptu M, Kim HT, Jacobsen E, Fisher DC, LaCasce A, Ho VT, Cutler CS, Koreth J, Soiffer RJ, Antin JH, Berliner N, Nikiforow S. Favorable outcomes following allogeneic transplantation in adults with hemophagocytic lymphohistiocytosis. Blood Adv. 2023 06 13; 7(11):2309-2316.

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Venigalla T, Kalathil S, Bansal M, Morginstin M, Jorge V, Perosio P. An Unusual Case of Hemophagocytic Lymphohistiocytosis Associated with Mycobacterium chimaera or Large-Cell Neuroendocrine Carcinoma. Curr Oncol. 2023 03 21; 30(3):3529-3536.

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Nagai H, Kirino Y, Nakano H, Kunishita Y, Henmi R, Szymanski AM, Yoshimi R, Ombrello MJ, Nakajima H. Elevated serum gasdermin D N-terminal implicates monocyte and macrophage pyroptosis in adult-onset Still's disease. Rheumatology (Oxford). 2021 08 02; 60(8):3888-3895.

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Benavides N, Spessott WA, Sanmillan ML, Vargas M, Livingston MS, Erickson N, Pozos TC, McCormick ME, Scharrig E, Messinger YH, Giraudo CG. STXBP2-R190C Variant in a Patient With Neonatal Hemophagocytic Lymphohistiocytosis (HLH) and G6PD Deficiency Reveals a Critical Role of STXBP2 Domain 2 on Granule Exocytosis. Front Immunol. 2020; 11:545414.

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Salama HA, Jazieh AR, Alhejazi AY, Absi A, Alshieban S, Alzahrani M, Alaskar A, Gmati G, Damlaj M, Abuelgasim KA, Alghamdi A, Alahmari B, Almugairi A, Alzahrani H, Bazarbachi A, Musa MOH, Goyal G. Highlights of the Management of Adult Histiocytic Disorders: Langerhans Cell Histiocytosis, Erdheim-Chester Disease, Rosai-Dorfman Disease, and Hemophagocytic Lymphohistiocytosis. Clin Lymphoma Myeloma Leuk. 2021 01; 21(1):e66-e75.

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Prokesch BC, Nagalla S, Ezzati F, Tujios SR, Dominguez A, Chen W, Kershaw C, Patel P, de la Flor C, Foster J, Martin AA, de la Morena MT, Wysocki CA. What's in a name? The heterogeneous clinical spectrum and prognostic factors in a cohort of adults with hemophagocytic lymphohistiocytosis. Transfus Apher Sci. 2018 Dec; 57(6):779-784.

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Merrill SA, Naik R, Streiff MB, Shanbhag S, Lanzkron S, Braunstein EM, Moliterno AM, Brodsky RA. A prospective quality improvement initiative in adult hemophagocytic lymphohistiocytosis to improve testing and a framework to facilitate trigger identification and mitigate hemorrhage from retrospective analysis. Medicine (Baltimore). 2018 Aug; 97(31):e11579.

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