Idiopathic Pulmonary Fibrosis

"Idiopathic Pulmonary Fibrosis" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus, MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure, which enables searching at various levels of specificity.

MeSH information

Definition | Details | More General Concepts | Related Concepts | More Specific Concepts

A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

Descriptor ID	D054990
MeSH Number(s)	C08.381.483.487.500 C08.381.765.500
Concept/Terms	Idiopathic Pulmonary Fibrosis Idiopathic Pulmonary Fibrosis Idiopathic Pulmonary Fibroses Pulmonary Fibroses, Idiopathic Familial Idiopathic Pulmonary Fibrosis Fibrocystic Pulmonary Dysplasia Dysplasia, Fibrocystic Pulmonary Dysplasias, Fibrocystic Pulmonary Fibrocystic Pulmonary Dysplasias Pulmonary Dysplasia, Fibrocystic Pulmonary Dysplasias, Fibrocystic Fibrosing Alveolitis, Cryptogenic Hamman-Rich Disease Disease, Hamman-Rich Diseases, Hamman-Rich Hamman Rich Disease Hamman-Rich Diseases Interstitial Pneumonitis, Usual Interstitial Pneumonitides, Usual Pneumonitides, Usual Interstitial Pneumonitis, Usual Interstitial Usual Interstitial Pneumonitides Usual Interstitial Pneumonitis Pulmonary Fibrosis, Idiopathic Usual Interstitial Pneumonia Interstitial Pneumonia, Usual Interstitial Pneumonias, Usual Usual Interstitial Pneumonias Idiopathic Fibrosing Alveolitis, Chronic Form Cryptogenic Fibrosing Alveolitis Cryptogenic Fibrosing Alveolitides Fibrosing Alveolitides, Cryptogenic Idiopathic Pulmonary Fibrosis, Familial

Below are MeSH descriptors whose meaning is more general than "Idiopathic Pulmonary Fibrosis".

Diseases [C]
Respiratory Tract Diseases [C08]
Lung Diseases [C08.381]
Lung Diseases, Interstitial [C08.381.483]
Idiopathic Interstitial Pneumonias [C08.381.483.487]
Idiopathic Pulmonary Fibrosis [C08.381.483.487.500]
Pulmonary Fibrosis [C08.381.765]
Idiopathic Pulmonary Fibrosis [C08.381.765.500]

Below are MeSH descriptors whose meaning is related to "Idiopathic Pulmonary Fibrosis".

Below are MeSH descriptors whose meaning is more specific than "Idiopathic Pulmonary Fibrosis".

publications

Timeline | Most Recent

This graph shows the total number of publications written about "Idiopathic Pulmonary Fibrosis" by people in this website by year, and whether "Idiopathic Pulmonary Fibrosis" was a major or minor topic of these publications.

Bar chart showing 30 publications over 13 distinct years, with a maximum of 4 publications in 2019 and 2024

To see the data from this visualization as text, click here.

Year	Major Topic	Minor Topic	Total
2009	2	1	3
2011	1	0	1
2014	1	0	1
2015	1	0	1
2016	0	2	2
2017	3	0	3
2018	2	0	2
2019	3	1	4
2020	2	0	2
2021	3	0	3
2022	1	0	1
2023	3	0	3
2024	2	2	4

Below are the most recent publications written about "Idiopathic Pulmonary Fibrosis" by people in Profiles.

Salisbury ML, Markin C, Fadely T, Guttentag AR, Humphries SM, Lynch DA, Kropski JA, Blackwell TS. Progressive Early Interstitial Lung Abnormalities in Persons at Risk for Familial Pulmonary Fibrosis: A Prospective Cohort Study. Am J Respir Crit Care Med. 2024 12 15; 210(12):1441-1452.

View in: PubMed
Salisbury ML, Markin CR, Fadely TH, Guttentag AR, Kropski JA, Blackwell TS. Impact of the COVID-19 Pandemic on a Program to Screen for Subclinical Familial Pulmonary Fibrosis. Am J Respir Crit Care Med. 2024 09 01; 210(5):669-672.

View in: PubMed
Kulkarni T, Criner GJ, Kass DJ, Rosas IO, Scholand MB, Dilling DF, Summer R, Duncan SR. Design of the STRIVE-IPF trial- study of therapeutic plasma exchange, rituximab, and intravenous immunoglobulin for acute exacerbations of idiopathic pulmonary fibrosis. BMC Pulm Med. 2024 Mar 20; 24(1):143.

View in: PubMed
Summer R, Todd JL, Neely ML, Lobo LJ, Namen A, Newby LK, Shafazand S, Suliman S, Hesslinger C, Keller S, Leonard TB, Palmer SM, Ilkayeva O, Muehlbauer MJ, Newgard CB, Roman J. Circulating metabolic profile in idiopathic pulmonary fibrosis: data from the IPF-PRO Registry. Respir Res. 2024 Jan 25; 25(1):58.

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Zhao J, Fares J, George G, Maheu A, Loizidis G, Roman J, Kramer D, Li M, Summer R. Racial and ethnic disparities in antifibrotic therapy in idiopathic pulmonary fibrosis. Respirology. 2023 11; 28(11):1036-1042.

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George G, Kramer D, Summer R. Diagnostic unification of usual interstitial pneumonia is a step back. Lancet Respir Med. 2023 06; 11(6):e53.

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Kramer D, George G, Summer R. Moving senolytics closer to the clinic in IPF. EBioMedicine. 2023 04; 90:104513.

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Ritzenthaler JD, Torres-Gonzalez E, Zheng Y, Zelko IN, van Berkel V, Nunley DR, Kidane B, Halayko AJ, Summer R, Watson WH, Roman J. The profibrotic and senescence phenotype of old lung fibroblasts is reversed or ameliorated by genetic and pharmacological manipulation of Slc7a11 expression. Am J Physiol Lung Cell Mol Physiol. 2022 03 01; 322(3):L449-L461.

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Shaghaghi H, Cuevas-Mora K, Para R, Tran C, Roque W, Robertson MJ, Rosas IO, Summer R, Romero F. A model of the aged lung epithelium in idiopathic pulmonary fibrosis. Aging (Albany NY). 2021 07 08; 13(13):16922-16937.

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Sharma P, Alizadeh J, Juarez M, Samali A, Halayko AJ, Kenyon NJ, Ghavami S, Zeki AA. Autophagy, Apoptosis, the Unfolded Protein Response, and Lung Function in Idiopathic Pulmonary Fibrosis. Cells. 2021 06 30; 10(7).

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